hypoplastic right ventricle with multiple associated anomaly: a challenging case for biventricular repair or univentricular approach?

نویسندگان

anita sadeghpour echocardiography research center, rajaie cardiovascular medical and research center, iran university medical science, tehran, ir iran; md, fase, facc, echocardiography research center, rajaie cardiovascular medical and research center, tehran, ir iran. tel: +98-2123922145, fax: +98-2122042026

majid kyavar rajaie cardiovascular medical and research center, iran university medical science, tehran, ir iran

mohammad ali yousefnia rajaie cardiovascular medical and research center, iran university medical science, tehran, ir iran

soheila chamanian mashhad university medical sciences, mashhad, ir iran

چکیده

abstract hypoplastic right ventricular is a rare congenital heart disease. a few cases have been reported. we presented a case with hypoplastic right ventricular and multiple associated anomaly (ventricular septal defect, atrial septal defect and pulmonary stenosis) in whom the main concern was whether biventricular repair or fontan type surgery would be the optimal management in this patient. biventricular repair was done successfully using the multimodality cardiac imaging with intraoperative transesophageal echocardiography.

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عنوان ژورنال:
archives of cardiovascular imaging

جلد ۱، شماره ۱، صفحات ۳۱-۳

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